productdatasheet
CatalogNo.:13808
Size:50ugpeptideimmunogenaffinitypurifiedantibodyinPBScontaining0.1%sodiumazide.
Glycogenphosphorylase(GP)removesandconvertsoneglucosemoleculefromglycogentoglucose-1-phosphate.
MammalianGPsarefoundinatleastthreeisozymicformsthataredistinguishedbyfunctionalandstructuralpropertiesaswellasbythetissuesinwhichtheyarepreferentiallyexpressed.Inmuscle,glycogenprovidesglucoseforenergyproductionduringexercise.Glycogenstoragedisease(alsoknownasMcArdle’sdisease)isaformofautosomalrecessivemyopathythatisresponsIBLeforthelackofactivityofmuscleGPandischaracterizedbyexerciseintolerance,musclecramps,andrecurrentmyo-globinuria.
Antigen:SyntheticpeptideconjugatedtoKLH.
HostSpecies:Rabbit
Preservatives:0.1%sodiumazide
SPECIFICITYThisantibodyrecognizestheC-terminaldomainofhumanmuscleGP.
Immunohistochemistry:Useat20ug/ml.
Skeletalmuscle:Formalin-fixed,paraffin-embedded
DiluteinPBSormediumwhichisidenticaltothatusedintheassaysystem.
Thisantibodyisstableat4oC(short-term)and-70oC(long-term).
Forinvitroinvestigationaluseonly.Notforuseintherapeuticordiagnosticprocedures.
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